Introduction and Objectives:
Congenital anomalies are characterized by structural or functional changes that occur during intrauterine life and can be identified before or at birth, or later in life. Approximately 50% cannot be linked to a specific cause, however, known causes include: genetic, infectious, nutritional, environmental, multifactorial factors. An estimated that these anomalies represent 6% of births in the world and 0.7% in Brazil. The objective is to evaluate the epidemiological profile of congenital anomalies registered in the Live Birth Information System (SINASC) of the city of Campo Bom, localized of the state of Rio Grande do Sul, Brazil.

Methods:
In Brazil, the notification of congenital anomaly is performed in the SINASC. Annually, approximately 24,000 newborns are registered in Brazil with some congenital anomalies. The data were evaluated from January/2012 to August/2022 through quantitative analysis.

Results:
In almost 10 years, 7,757 children were born in Campo Bom, of which 84 were diagnosed with congenital anomaly and of these 14 died. The information on congenital anomaly was blank and ignored at 11 and 16 times, respectively. Congenital anomalies with higher prevalence in the city are: unspecified polydactyly, other congenital deformities of the foot, unspecified hypospadia, unspecified congenital deformity of the foot, Down syndrome, other defects of upper limb reduction.

Conclusion:
The information regarding congenital anomalies is under reported, there is failure in the records, and the diagnosis at birth is quite heterogeneous in different regions of the country. It’s necessary to improve the records in the SINASC, strengthening the notification of these diseases to obtain more subsidies and improve the surveillance of congenital anomalies. In addition, we need to provide guidance on the measures to prevent these injuries, since 50% less can be prevented.